Compositions and methods of treating facioscapulohumeral muscular dystrophy
Patent Information
- Application Number
- IL311452
- Authority / Receiving Office
- IL · IL
- Patent Type
- Patents
- Current Assignee / Owner
- Priority Date
- 2021-09-16
- Filing Date
- 2022-09-15
- Publication Date
- 2026-07-01
- Estimated Expiration
- 2042-09-15
AI Technical Summary
Facioscapulohumeral muscular dystrophy (FSHD) lacks effective treatments, primarily due to the aberrant expression of the DUX4 gene leading to inappropriate protein presence, causing progressive skeletal muscle loss and weakness without approved therapeutic options.
A polynucleic acid molecule conjugate is developed, comprising an antibody or antigen binding fragment conjugated to a polynucleic acid that hybridizes to the DUX4 target sequence, mediating RNA interference to reduce DUX4 mRNA expression, thereby addressing the root cause of muscle pathology.
The polynucleic acid conjugate effectively reduces DUX4 mRNA transcript levels by at least 50% in muscle cells, modulating muscle atrophy and dystrophy symptoms, providing a potential disease-modifying therapeutic approach for FSHD.